Idiopathic interstitial pneumonia
Idiopathic interstitial pneumonia | |
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File:Usual interstitial pneumonia (1).JPG
Micrograph of usual interstitial pneumonia (UIP). UIP is the most common pattern of idiopathic interstitial pneumonia and usually represents idiopathic pulmonary fibrosis. H&E stain. Autopsy specimen.
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Classification and external resources | |
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Patient UK | Idiopathic interstitial pneumonia |
Idiopathic interstitial pneumonia (IIP), or noninfectious pneumonia[1] are a class of diffuse lung diseases. These diseases typically affect the pulmonary interstitium, although some also have a component affecting the airways (for instance, Cryptogenic organizing pneumonitis). There are seven recognized distinct subtypes of IIP.
Histologic classification
Classification can be complex,[2] and the combined efforts of clinicians, radiologists, and pathologists can help in the generation of a more specific diagnosis.[3][4]
Idiopathic interstitial pneumonia can be subclassified based on histologic appearance into the following patterns:[5][6]
Histology | Clinical Correlates |
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Desquamative interstitial pneumonia (DIP) | DIP |
Diffuse alveolar damage (DAD) | ARDS, AIP, TRALI |
Nonspecific interstitial pneumonia (NSIP) | NSIP |
Respiratory bronchiolitis | RB-ILD |
Usual interstitial pneumonia (UIP) | CVD, IPF, drug toxicity, pneumoconiosis |
Organizing pneumonia | Cryptogenic organizing pneumonia |
Lymphoid interstitial pneumonia (LIP) | LIP |
Usual interstitial pneumonia is the most common type.[7]
Development
Table 1: Development of the (histologic) idiopathic interstitial pneumonia classification
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UIP=usual interstitial pneumonia; DAD=diffuse alveolar damage; NSIP=non-specific interstitial pneumonia; DIP=desquamative interstitial pneumonia; RB=respiratory bronchiolitis; BIP=bronchiolitis obliterans interstitial pneumonia; OP=organizing pneumonia; LIP=lymphoid interstitial pneumonia; LPD=lymphoproliferative disease (not considered a diffuse lung disease); GIP=giant cell interstitial pneumonia; HMF=heavy metal fibrosis, no longer grouped with diffuse lung disease
Lymphoid interstitial pneumonia was originally included in this category, then excluded, then included again.[8]
References
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- ↑ Leslie KO, Wick MR. Practical Pulmonary Pathology: A Diagnostic Approach. Elsevier Inc. 2005. ISBN 978-0-443-06631-3.
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