Idiopathic interstitial pneumonia

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Idiopathic interstitial pneumonia
File:Usual interstitial pneumonia (1).JPG
Micrograph of usual interstitial pneumonia (UIP). UIP is the most common pattern of idiopathic interstitial pneumonia and usually represents idiopathic pulmonary fibrosis. H&E stain. Autopsy specimen.
Classification and external resources
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Patient UK Idiopathic interstitial pneumonia
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Idiopathic interstitial pneumonia (IIP), or noninfectious pneumonia[1] are a class of diffuse lung diseases. These diseases typically affect the pulmonary interstitium, although some also have a component affecting the airways (for instance, Cryptogenic organizing pneumonitis). There are seven recognized distinct subtypes of IIP.

Histologic classification

Classification can be complex,[2] and the combined efforts of clinicians, radiologists, and pathologists can help in the generation of a more specific diagnosis.[3][4]

Idiopathic interstitial pneumonia can be subclassified based on histologic appearance into the following patterns:[5][6]

Histology Clinical Correlates
Desquamative interstitial pneumonia (DIP) DIP
Diffuse alveolar damage (DAD) ARDS, AIP, TRALI
Nonspecific interstitial pneumonia (NSIP) NSIP
Respiratory bronchiolitis RB-ILD
Usual interstitial pneumonia (UIP) CVD, IPF, drug toxicity, pneumoconiosis
Organizing pneumonia Cryptogenic organizing pneumonia
Lymphoid interstitial pneumonia (LIP) LIP

Usual interstitial pneumonia is the most common type.[7]

Development

Table 1: Development of the (histologic) idiopathic interstitial pneumonia classification

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UIP=usual interstitial pneumonia; DAD=diffuse alveolar damage; NSIP=non-specific interstitial pneumonia; DIP=desquamative interstitial pneumonia; RB=respiratory bronchiolitis; BIP=bronchiolitis obliterans interstitial pneumonia; OP=organizing pneumonia; LIP=lymphoid interstitial pneumonia; LPD=lymphoproliferative disease (not considered a diffuse lung disease); GIP=giant cell interstitial pneumonia; HMF=heavy metal fibrosis, no longer grouped with diffuse lung disease

Lymphoid interstitial pneumonia was originally included in this category, then excluded, then included again.[8]

References

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  5. Leslie KO, Wick MR. Practical Pulmonary Pathology: A Diagnostic Approach. Elsevier Inc. 2005. ISBN 978-0-443-06631-3.
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